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| 신기능 움직이애를 동반한 Hereditary Coproporphyria 1예 |
| 강재황 , 함종렬 , 정판준 , 김성욱 , 심대석 , 김정렬 , 김호철 , 이근홍 , 황일용 |
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| Abstract |
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We report a case of hereditary coproporphyria with renal insufficiency in a 20 years old girl who had frequent abdominal pain. The typical clinical and biochem- ical findings of hepatic porphyria represent the heredi- tary coproporphyria, most likely. Her symptoms and signs were clearly exacerbated in a relation to the menstrual cycle. During admission, serum creatinine changed up to 3 8 mg/dl. Until 35 days after discharge, she was found to have persistently elevated serum creatinine concentration. On the renal biopsy, there was chronic Tubulo-Interstitial Nephritis, which presented with focal and mild degree interstitial edema, chronic inflammatory cells infiltrtion, and vacuolization of tubular cells. Possible etiologic factors including porphyria or its precursor itself for the renal insufficiency of this patient (HCP) should be discussed. |
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