| A Case of Idiopathic Retroperitoneal Fibrosis Associated with Rapidly Progressive Glomerulonephritis with Anti-myeloperoxidase Antineutrophil Cytoplasmic Antibodies |
| Yu-Ji Lee, M.D., Hae Won Jung, M.D., Jung Eun Lee, M.D., Wooseong Huh, M.D., Dae Joong Kim, M.D., Ha Young Oh, M.D. and Yoon Goo Kim, M.D. |
| Department of Medicine, Samsung Medical Center Sungkyunkwan University School of Medicine, Seoul, Korea |
| 증례 : 혈Anti-myeloperoxidase antineutrophil cytoplasmic antibodies 양성의 급속진행성 사구체신염이 동반된 후복막 섬유증식증 1예 |
| 이유지, 정혜원, 이정은, 허우성, 김대중, 오하영, 김윤구 |
| 성균관대학교 의과대학 삼성서울병원 신장내과 |
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| Abstract |
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Idiopathic retroperitoneal fibrosis is a rare disease characterized by the presence of retroperitoneal fibroinflammatory tissue, which often surrounds the abdominal aorta, the ureters, or other abdominal organs. There have been sporadic reports of an association with autoimmune diseases, although the pathogenesis of idiopathic retroperitoneal fibrosis is unclear. However, there are very few reports ofidiopathic retroperitoneal fibrosis associated with rapidly progressive glomerulonephritis. We report a case with idiopathic retroperitoneal fibrosis associated with rapidly progressive glomerulonephritis, and anti-myeloperoxidase antineutrophil cytoplasmic antibodies (anti MPO-ANCA), that was improved by the combination therapy of steroids and cyclophosphamide. |
| Key Words:
Retroperitoneal fibrosis, Glomerulonephritis, Antineutrophil cytoplasmic antibodies |
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