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| 용혈성요독증후군을 동반한 Multicentric Angiofollicular Lymph Node Hyperplasia 1예 |
| 이상구 , 박민선 , 한동철 , 이희발 , 유병희 , 이동화 |
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| Abstract |
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MFAH resembles classic AFH histologically but is characterized by multicentric lymphadenopathy, severe systemic manifestations and aggressive clinical course. MAFH is occasionally associated with other dis- orders, such as myasthenia gravis, nephrotic syndrome, thrombotic thrombocytopenic purpura, peripheral neur- opathy, renal failure, and hyperimmune syndrome. We report a case of hemolytic uremic syndrome and acute renal failure associated with MAFH. A 41 year old man presented with acute renal failure and showed systemic manifestations such as fever, weight loss, sweat, multicentric lymphadenopathy, hepatos- plenomegaly, Jaundice, serositis, anemia, throm- bocytopenia, polyclonal hypergammaglobulinemia, in- creased ESR, rouleau formation in PBS, enterococalintraabdominal abscess and pseudomonas septicemia in the course of the disease. Kidney biopsy sho ived hemolytic-uremia syndrome and lymph node biopsy showed mixed type of AFH. |
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